Las Glucogenosis en España: Situación Actual y Guías Informativas



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6. AGRADECIMIENTOS

Este trabajo no habría sido posible sin la ayuda y constante apoyo de mis pa-


dres; José y Carmen, y hermanos, Ma Carmen y José, a quien les estaré eterna-
mente agradecido.

También quisiera agradecer la inestimable ayuda de la Prof. Ana Gago Martí-


nez, de la Universidad de Vigo, que puso todos los medios necesarios para la re-
alización del estudio y del Dr. Ricardo V. García-Mayor García, del Complejo
Hospitalario Xeral-Cíes de Vigo, por sus interesantes y útiles comentarios.

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Las Glucogenosis en España



BIBLIOGRAFÍA

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    965, McGraw-Hill Inc., New York.

  2. Chou J.Y. The Molecular Basis of Type 1 Glycogen Storage Diseases. Curr.
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  3. Foster J.D.,Nordlie R.C.The Biochemistry and Molecular Biology of the GIu-
    cose-6-Phosphatase System. Exp. Biol. Med., 2002; 227(8): 601-608.

  4. Lei K.J., Shelly L.L., Lin B., Sidbury J.B., Chen Y.-T., Nordlie R.C., Chou
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  5. Lin B., Hiraiwa H., Pan C.J., Nordlie R.C.Chou J.Y.Type lc glycogen stor-
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  6. Chou J. Y., Matern D. Mansfield B .C, Chen Y.-T. Type I glycogen storage diseases:
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  13. Narisawa K., Igarashi Y., Otomo H.,Tada K. A new variant of glycogen stor-
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  14. Lange A.J., Arion W.J., Beaudet A.L. Type Ib glycogen storage disease is
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  1. Nordlic R.C., Sukalski K.A., Muñoz J.J., Baldwin J.J. Type le, a novel
    glycogenosis. Underlying mechanisms. J. Biol. Chem., 1983; 258: 9739.

  2. Janecke A.R., Bosshard N.U., Mayatepek E., Schulze A., Gitzelmann R.,
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  3. Marcolongo P.. Banhegyi G., Benedetti A, Hinds C.J., Burchell A. Liver mi-
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  4. Rake J.P.. ten Berge A.M., Visser G., Verlind E., Niezen-Koning K.E., Buys
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  6. Smit G.P.A. The long-term outcome of patientes with glycogen storage disease
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  8. Bier D.M., Leake R.D., Haymond M.W., Arnold K.J., Gruenke L.D., Sperling
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  10. Veiga da Cunha M., Gerin I., Schaftingen E. How many forms of glycogen
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  11. Chou J.Y., Zingone A., Pan C.-J. Adenovirus-mediated gene therapy in a
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  12. Sun M.-S.,Pan C.-J..ShiehJ.-J.,Ghosh A.,Chen L.-Y.,Mansfield B.C.,Ward
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  13. Visser G., Rake J. P., Labrune P., Leonard J. V., Moses S., Ullrich K., Wendel
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